AFG3L2 Mouse Monoclonal Antibody [Clone ID: OTI4B6]
CAT#: TA504858S
AFG3L2 mouse monoclonal antibody, clone OTI4B6 (formerly 4B6)
Size: 100 ul
View other "OTI4B6" antibodies (4)
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CNY 800.00
Cited in 1 publication. |
CNY 300.00
CNY 1,430.00
CNY 3,080.00
Specifications
Product Data | |
Clone Name | OTI4B6 |
Applications | WB |
Recommend Dilution | WB 1:2000 |
Reactivity | Human, Mouse, Rat |
Host | Mouse |
Clonality | Monoclonal |
Immunogen | Human recombinant protien fragment corresponding to amino acids 1-250 of human AFG3L2(NP_006787) produced in E.coli. |
Formulation | PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide. |
Concentration | 1 mg/ml |
Purification | Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G) |
Conjugation | Unconjugated |
Storage Condition | Store at -20°C as received. |
Predicted Protein Size | 88.3 kDa |
Gene Name | AFG3 like matrix AAA peptidase subunit 2 |
Database Link | |
Background | This gene encodes a protein localized in mitochondria and closely related to paraplegin. The paraplegin gene is responsible for an autosomal recessive form of hereditary spastic paraplegia. This gene is a candidate gene for other hereditary spastic paraplegias or neurodegenerative disorders. [provided by RefSeq, Jul 2008] |
Synonyms | SCA28; SPAX5 |
Reference Data | |
Protein Families | Druggable Genome, Protease, Transmembrane |
Citations (1)
The use of this Antibodies has been cited in the following citations: |
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Pathogenic variants in the AFG3L2 proteolytic domain cause SCA28 through haploinsufficiency and proteostatic stress-driven OMA1 activation
,Tulli, S;Del Bondio, A;Baderna, V;Mazza, D;Codazzi, F;Pierson, TM;Ambrosi, A;Nolte, D;Goizet, C;Toro, C;Baets, J;Deconinck, T;DeJonghe, P;Mandich, P;Casari, G;Maltecca, F;,
J. Med. Genet.
,PubMed ID 30910913
[AFG3L2]
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Other Versions
SKU | Description | Size | Price |
---|---|---|---|
CF504858 | Carrier-free (BSA/glycerol-free) AFG3L2 mouse monoclonal antibody, clone OTI4B6 (formerly 4B6) |
CNY 3,999.00 |
|
TA504858 | AFG3L2 mouse monoclonal antibody, clone OTI4B6 (formerly 4B6) |
CNY 1,999.00 |
|
TA504858AM | AFG3L2 mouse monoclonal antibody,clone 4B6, Biotinylated |
CNY 3,990.00 |
|
TA504858BM | AFG3L2 mouse monoclonal antibody,clone 4B6, HRP conjugated |
CNY 3,990.00 |