DNAH2 Mouse Monoclonal Antibody [Clone ID: 13H6]

CAT#: TA355286

Dystrophin Mouse Monoclonal Antibody



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CNY 20,746.00


货期*
7周

规格
    • 1 ml

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Specifications

Product Data
Clone Name 13H6
Applications IHC
Recommend Dilution 1:10 - 1:20
Reactivity Human
Host Mouse
Clonality Monoclonal
Immunogen Prokaryotic recombinant protein corresponding to a region of the rod domain of the human dystrophin molecule
Specificity Human dystrophin molecule
Formulation Lyophilized tissue culture supernatant containing 15 mM sodium azide as a preservative.
Reconstitution Method The user is required to reconstitute the contents of the vial with the correct volume of sterile distilled water as indicated on the vial label
Conjugation Unconjugated
Storage Condition Store at 2-8°C
Gene Name dynein, axonemal, heavy polypeptide 2
Background Duchenne Muscular dystrophy (DMD) is the most common of the muscular dystrophies resulting in progressive muscular wasting and death. Dystrophin is the 427kD protein product of the DMD gene located on the X chromosome at position Xp21. Abnormalities in protein expression occur in patients with DMD/BMD and dystrophin analysis may be used to distinguish these conditions from other neuromuscular diseases. Severe Duchenne muscular dystrophy is associated with a marked dystrophin deficiency, whereas patients with the milder form of Becker muscular dystrophy show less pronounced abnormalities of protein expression. The immunolabeling patterns for DYS1, DYS2 and DYS3 are similar; however, the use of all three antibodies is recommended to avoid the possibility of occasional false negative results.
Reference Data
*Delivery time may vary from web posted schedule. Occasional delays may occur due to unforeseen complexities in the preparation of your product. International customers may expect an additional 1-2 weeks in shipping.
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