GALNS (BC018027) Human Untagged Clone
CAT#: SC106153
(untagged)-Homo sapiens, Similar to galactosamine (N-acetyl)-6-sulfate sulfatase (Morquio syndrome, mucopolysaccharidosis type IVA), clone IMAGE:4796652
CNY 11,210.00
货期*
3周
规格
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经常一起买 (4)
Rabbit Polyclonal antibody to GALNS (galactosamine (N-acetyl)-6-sulfate sulfatase)
CNY 6,281.00
Specifications
Product Data | |
Type | Human Untagged Clone |
Tag | Tag Free |
Synonyms | GalN6S; GALNAC6S; GAS; MPS4A |
Vector | pCMV6-XL4 |
E. coli Selection | Ampicillin (100 ug/mL) |
Mammalian Cell Selection | None |
Sequence Data |
>NCBI ORF sequence for BC018027, the custom clone sequence may differ by one or more nucleotides
GTCGAGGCCCCGCCCCGCAGCCCAGCCGGAAGGGCCGGCGGACGCTCGCTAGGTCGGCTCGCTGGCCGGG GCTCCGCGGCTCCCGTGGTTGCCATGGCGGCGGTTGTCGCGGCGACGAGGTGGTGGCAGCTGTTGCTGGT GCTCAGCGCCGCGGGGATGGGGGCCTCGGGCGCCCAGCAGCCCCCCAACATCCTGCTCCTGCTCATGGAC GACGAATCACTCCCGCCACCTCGGGCCGCCGGGTCCCCCCGCTGGGCTCGAGTCTTACCTGACGGCTGTC TCTGTCCTCTGGAGAATGCTGAGCGAAGTGACTGCTTTCCAGAGCACGCTCTCCAGCGCCCAGGGGTCCG TGTCCTGACAGCAGTAGCCGGGCCTTTCTCTGCACTGAGTGGCATCTCCCTCCTAAAGATACTTTGCTTC AGAATTTCATCCTTTCACTTTTGAAGTTCCTCTGGGCCAGTGTAGATACTTTGTTTCAGAATTTCTTCTT TTCATTGTGTAACTCCTTCTGGGCCAGCATAGCTTCGCTGGATGAGCTGGGCTCTGCAGGTGAAGCCTCC CTGTTAAGTTTCTGCTTTTCCTGACTTTCTCAGAGGACAGAGGGGTGAGGCGGGGCAGCTCATGAATAAT TTTTTATGTTGAAGACTTGTCGAAATAATATTTTGGTTATGTTGGGTTAAATAAAATATAAAGTTAGTCT GTAAAAAAAAAAAAAAAAAAAGAAAAAAAAAAAAAAA >OriGene 5' read for BC018027 unedited
GGGGGGNGGGGNNNNNNNNNNNNNCCCNNNNCCGGTTCAGAATTTGTATACGACTCACTA TAGGCGGCCGCGNATTCGGCACCAGGCTAGGTCGGCTCGCTGGCCGGGGCTCCGCGGCTC CCGTGGTTGCCATGGCGGCGGTTGTCGCGGCGACGAGGTGGTGGCAGCTGTTGCTGGTGC TCAGCGCCGCGGGGATGGGGGCCTCGGGCGCCCCGCAGCCCCCCAACATCCTGCTCCTGC TCATGGACGACATGAAGGATTTGGGGGCAGAGCACTTGGCAGGTCATGAAGGGGTCCAAC TTCTCGGGTTGTTGAACGTCTACCTGGAACAAGAAGAGAGATTCCAACCTCGAGAAAAAG GGCTGAGTTTGATTGAGGCTACCCCGGAGAATGATAACACTTTGTGTCCAGGATTGAGAA ATGCCAAAGTTGAAGATTTAAGGAGTTTAGCCAACTTTTTTGGATCTTGCACTGAAACTT TTGTCCTGGCTGTCAATATTTTGGACAGGTTCTTGGCTCTTATGAAGGTGAAACCTAAAC ATTTGTCTTGCATTGGAGTCTGTTCTTTTTTGCTGGCTGCTAGAATAGTTGAAGAAGACT GCAATATTCCATCCACTCATGATGTGATCCGGATTAGTCAGTGTAAATGTACTGCTTCTG ACATAAAACGGATGGAAAAAATAATTTCAGAAAAATTGCACTATGAATTGGAAGCTACTA CTGCCTTNAACTNTNTGCACTTATACCATACTATTATACTNTGTCATACTTCAGAAAGGA AGAAATACTGAGCCTTTGATAACTAGAAGCTCAGCTNGAAGCTTTGCACTGCCGACTCAT CTTTTCAAAGCAAACCATCTGTATTAGCCTTGTGCCTCTCATTTTTGAAGTGGAAACTTT GAAAATCTGTGNAATACTGGNAANTCTCTTGCTAGTTAA |
Restriction Sites | NotI-NotI |
ACCN | BC018027 |
Insert Size | 2650 bp |
OTI Disclaimer | Our molecular clone sequence data has been matched to the reference identifier above as a point of reference. Note that the complete sequence of our molecular clones may differ from the sequence published for this corresponding reference, e.g., by representing an alternative RNA splicing form or single nucleotide polymorphism (SNP). |
Product Components | The ORF clone is ion-exchange column purified and shipped in a 2D barcoded Matrix tube containing 10ug of transfection-ready, dried plasmid DNA (reconstitute with 100 ul of water). |
Reconstitution | 1. Centrifuge at 5,000xg for 5min. 2. Carefully open the tube and add 100ul of sterile water to dissolve the DNA. 3. Close the tube and incubate for 10 minutes at room temperature. 4. Briefly vortex the tube and then do a quick spin (less than 5000xg) to concentrate the liquid at the bottom. 5. Store the suspended plasmid at -20°C. The DNA is stable for at least one year from date of shipping when stored at -20°C. |
Reference Data | |
RefSeq | BC018027.1 |
RefSeq Size | 737 bp |
RefSeq ORF | 737 bp |
Locus ID | 2588 |
Protein Families | Druggable Genome |
Protein Pathways | Glycosaminoglycan degradation, Lysosome, Metabolic pathways |
Gene Summary | This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans, keratan sulfate, and chondroitin 6-sulfate. Sequence alterations including point, missense and nonsense mutations, as well as those that affect splicing, result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome, a lysosomal storage disorder. [provided by RefSeq, Jul 2008] |
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